{"id":7317,"date":"2024-09-29T11:38:10","date_gmt":"2024-09-29T11:38:10","guid":{"rendered":"https:\/\/delta-medlab.com\/blog\/?p=7317"},"modified":"2024-09-29T14:59:57","modified_gmt":"2024-09-29T14:59:57","slug":"porphyria","status":"publish","type":"post","link":"https:\/\/delta-medlab.com\/blog\/porphyria\/","title":{"rendered":"\u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0646\u0638\u0631\u0629 \u0634\u0627\u0645\u0644\u0629 \u0639\u0644\u0649 \u0645\u0631\u0636 \u0646\u0627\u062f\u0631 \u064a\u0624\u062b\u0631 \u0639\u0644\u0649 \u0627\u0644\u0623\u0639\u0635\u0627\u0628 \u0648\u0627\u0644\u062c\u0644\u062f"},"content":{"rendered":"<p>\u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0647\u064a \u0645\u062c\u0645\u0648\u0639\u0629 \u0645\u0646 \u0627\u0644\u0623\u0645\u0631\u0627\u0636 \u0627\u0644\u0648\u0631\u0627\u062b\u064a\u0629 \u0627\u0644\u0646\u0627\u062f\u0631\u0629 \u0627\u0644\u062a\u064a \u062a\u0646\u062a\u062c \u0639\u0646 \u062e\u0644\u0644 \u0641\u064a \u0639\u0645\u0644\u064a\u0629 \u062a\u0635\u0646\u064a\u0639 \u0627\u0644\u0647\u064a\u0645 (heme)\u060c \u0648\u0647\u0648 \u0645\u0643\u0648\u0651\u0646 \u0636\u0631\u0648\u0631\u064a \u0644\u062e\u0644\u0627\u064a\u0627 \u0627\u0644\u062f\u0645 \u0627\u0644\u062d\u0645\u0631\u0627\u0621 \u0648\u0644\u0644\u0639\u062f\u064a\u062f \u0645\u0646 \u0627\u0644\u0625\u0646\u0632\u064a\u0645\u0627\u062a \u0641\u064a \u0627\u0644\u062c\u0633\u0645. \u064a\u0639\u0648\u062f \u0633\u0628\u0628 \u0647\u0630\u0627 \u0627\u0644\u062e\u0644\u0644 \u0625\u0644\u0649 \u0646\u0642\u0635 \u0641\u064a \u0627\u0644\u0625\u0646\u0632\u064a\u0645\u0627\u062a \u0627\u0644\u0645\u0633\u0624\u0648\u0644\u0629 \u0639\u0646 \u062a\u062d\u0648\u064a\u0644 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0646\u0627\u062a \u0625\u0644\u0649 \u0627\u0644\u0647\u064a\u0645\u060c \u0645\u0645\u0627 \u064a\u0624\u062f\u064a \u0625\u0644\u0649 \u062a\u0631\u0627\u0643\u0645 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0646\u0627\u062a \u0641\u064a \u0627\u0644\u062c\u0633\u0645 \u0627\u0644\u062a\u064a \u064a\u0645\u0643\u0646 \u0623\u0646 \u062a\u0633\u0628\u0628 \u0645\u062c\u0645\u0648\u0639\u0629 \u0645\u062a\u0646\u0648\u0639\u0629 \u0645\u0646 \u0627\u0644\u0623\u0639\u0631\u0627\u0636\u060c \u062a\u062a\u0639\u0644\u0642 \u0628\u0627\u0644\u062c\u0647\u0627\u0632 \u0627\u0644\u0639\u0635\u0628\u064a \u0648\u0627\u0644\u062c\u0644\u062f \u0648\u0627\u0644\u062c\u0647\u0627\u0632 \u0627\u0644\u0647\u0636\u0645\u064a \u0648\u062a\u062e\u062a\u0644\u0641 \u0628\u0627\u062e\u062a\u0644\u0627\u0641 \u0646\u0648\u0639 \u0627\u0644\u0645\u0631\u0636.<\/p>\r\n<p>\u062a\u0639\u062a\u0628\u0631 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0645\u0646 \u0627\u0644\u062d\u0627\u0644\u0627\u062a \u0627\u0644\u0645\u0639\u0642\u062f\u0629 \u0627\u0644\u062a\u064a \u062a\u062a\u0637\u0644\u0628 \u062a\u0634\u062e\u064a\u0635\u064b\u0627 \u062f\u0642\u064a\u0642\u064b\u0627 \u0648\u0625\u062f\u0627\u0631\u0629 \u0645\u062a\u062e\u0635\u0635\u0629\u060c \u062e\u0627\u0635\u0629\u064b \u0648\u0623\u0646 \u0623\u0639\u0631\u0627\u0636\u0647\u0627 \u0642\u062f \u062a\u062a\u0634\u0627\u0628\u0647 \u0645\u0639 \u0627\u0644\u0639\u062f\u064a\u062f \u0645\u0646 \u0627\u0644\u0623\u0645\u0631\u0627\u0636 \u0627\u0644\u0623\u062e\u0631\u0649. \u0641\u064a \u0647\u0630\u0627 \u0627\u0644\u0645\u0642\u0627\u0644\u060c \u0633\u0646\u0633\u062a\u0639\u0631\u0636 \u0623\u0648\u062c\u0647 \u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 \u0648\u0623\u0633\u0628\u0627\u0628\u0647 \u0648\u0623\u0639\u0631\u0627\u0636\u0647 \u0648\u0637\u0631\u0642 \u0627\u0644\u062a\u0639\u0627\u0645\u0644 \u0645\u0639\u0647.<\/p>\r\n<h2>\u0645\u0627 \u0647\u064a \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627\u061f<\/h2>\r\n<p>\u0647\u064a \u0627\u0636\u0637\u0631\u0627\u0628 \u0641\u064a \u062a\u0643\u0648\u064a\u0646 \u0627\u0644\u0647\u064a\u0645 \u0627\u0644\u0646\u0627\u062a\u062c \u0639\u0646 \u0637\u0641\u0631\u0627\u062a \u062c\u064a\u0646\u064a\u0629 \u062a\u0624\u062f\u064a \u0625\u0644\u0649 \u0646\u0642\u0635 \u0627\u0644\u0625\u0646\u0632\u064a\u0645\u0627\u062a \u0627\u0644\u0645\u0633\u0624\u0648\u0644\u0629 \u0639\u0646 \u0647\u0630\u0647 \u0627\u0644\u0639\u0645\u0644\u064a\u0629. \u0647\u0646\u0627\u0643 \u0639\u062f\u0629 \u0623\u0646\u0648\u0627\u0639 \u0645\u0646 \u0627\u0644\u0645\u0631\u0636 \u0645\u062b\u0644 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0627\u0644\u062d\u0627\u062f\u0629 \u0627\u0644\u0645\u062a\u0642\u0637\u0639\u0629 \u0648\u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0627\u0644\u062c\u0644\u062f\u064a\u0629 \u0648\u064a\u062e\u062a\u0644\u0641 \u0643\u0644 \u0646\u0648\u0639 \u0641\u064a \u0627\u0644\u0623\u0639\u0631\u0627\u0636 \u0648\u0622\u0644\u064a\u0629 \u0627\u0644\u062a\u0623\u062b\u064a\u0631.<\/p>\r\n<h3>\u0645\u0627 \u0647\u0648 \u0627\u0644\u0647\u064a\u0645 \u061f<\/h3>\r\n<p>\u0627\u0644\u0647\u064a\u0645 \u0647\u0648 \u062c\u0632\u0621 \u0645\u0646 \u0627\u0644\u0647\u064a\u0645\u0648\u063a\u0644\u0648\u0628\u064a\u0646 \u0627\u0644\u0630\u064a \u064a\u0648\u062c\u062f \u0641\u064a \u062e\u0644\u0627\u064a\u0627 \u0627\u0644\u062f\u0645 \u0627\u0644\u062d\u0645\u0631\u0627\u0621\u060c \u0648\u064a\u0633\u0627\u0639\u062f \u0641\u064a \u062d\u0645\u0644 \u0627\u0644\u0623\u0643\u0633\u062c\u064a\u0646. \u062a\u0624\u062f\u064a \u0627\u0644\u0637\u0641\u0631\u0627\u062a \u0625\u0644\u0649 \u062a\u0631\u0627\u0643\u0645 \u0645\u0631\u0643\u0628\u0627\u062a \u062a\u0633\u0645\u0649 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0646\u0627\u062a\u060c \u0623\u0648 \u0645\u0631\u0643\u0628\u0627\u062a \u0630\u0627\u062a \u0635\u0644\u0629 \u0641\u064a \u0627\u0644\u062c\u0633\u0645 \u0627\u0644\u062a\u064a \u0642\u062f \u062a\u0643\u0648\u0646 \u0633\u0627\u0645\u0629 \u0644\u0644\u0623\u0639\u0635\u0627\u0628 \u0623\u0648 \u062a\u0633\u0628\u0628 \u062d\u0633\u0627\u0633\u064a\u0629 \u0627\u0644\u062c\u0644\u062f \u0644\u0623\u0634\u0639\u0629 \u0627\u0644\u0634\u0645\u0633.<\/p>\r\n<p>&nbsp;<\/p>\r\n<h3>\u0645\u0627 \u0647\u064a \u0646\u0633\u0628\u0629 \u0627\u0646\u062a\u0634\u0627\u0631 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0641\u064a \u0627\u0644\u0634\u0631\u0642 \u0627\u0644\u0623\u0648\u0633\u0637\u061f<\/h3>\r\n<p>\u0646\u0633\u0628\u0629 \u0627\u0646\u062a\u0634\u0627\u0631 \u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 \u0641\u064a \u0645\u0646\u0637\u0642\u0629 \u0627\u0644\u0634\u0631\u0642 \u0627\u0644\u0623\u0648\u0633\u0637 \u063a\u064a\u0631 \u0645\u0648\u062b\u0642\u0629 \u0628\u0634\u0643\u0644 \u062f\u0642\u064a\u0642 \u0641\u064a \u0627\u0644\u0623\u062f\u0628\u064a\u0627\u062a \u0627\u0644\u0637\u0628\u064a\u0629 \u0645\u0642\u0627\u0631\u0646\u0629 \u064b\u0628\u0645\u0646\u0627\u0637\u0642 \u0623\u062e\u0631\u0649 \u0645\u062b\u0644 \u0623\u0648\u0631\u0648\u0628\u0627 \u0648\u0623\u0645\u0631\u064a\u0643\u0627 \u0627\u0644\u0634\u0645\u0627\u0644\u064a\u0629. \u0648\u0645\u0639 \u0630\u0644\u0643 \u062a\u064f\u0639\u062a\u0628\u0631 \u0645\u0646 \u0627\u0644\u0623\u0645\u0631\u0627\u0636 \u0627\u0644\u0646\u0627\u062f\u0631\u0629 \u0639\u0644\u0649 \u0645\u0633\u062a\u0648\u0649 \u0627\u0644\u0639\u0627\u0644\u0645\u060c \u062d\u064a\u062b \u062a\u0642\u062f\u0631 \u0646\u0633\u0628\u0629 \u0627\u0646\u062a\u0634\u0627\u0631\u0647\u0627 \u0628\u062d\u0648\u0627\u0644\u064a 1 \u0625\u0644\u0649 100,000 \u0634\u062e\u0635.<\/p>\r\n<p>\u062a\u0634\u064a\u0631 \u0628\u0639\u0636 \u0627\u0644\u062f\u0631\u0627\u0633\u0627\u062a \u0625\u0644\u0649 \u0623\u0646 \u0628\u0639\u0636 \u0623\u0634\u0643\u0627\u0644 \u0627\u0644\u0645\u0631\u0636 \u0645\u062b\u0644 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0627\u0644\u062c\u0644\u062f\u064a\u0629 \u0627\u0644\u0628\u0637\u064a\u0626\u0629 (Porphyria Cutanea Tarda)\u060c \u0642\u062f \u062a\u0643\u0648\u0646 \u0623\u0643\u062b\u0631 \u0627\u0646\u062a\u0634\u0627\u0631\u0627\u064b \u0641\u064a \u0628\u0639\u0636 \u0627\u0644\u0645\u0646\u0627\u0637\u0642 \u0627\u0644\u062c\u063a\u0631\u0627\u0641\u064a\u0629 \u0646\u062a\u064a\u062c\u0629 \u0644\u0639\u0648\u0627\u0645\u0644 \u0648\u0631\u0627\u062b\u064a\u0629 \u0648\u0627\u0644\u062a\u0639\u0631\u0636 \u0644\u0645\u0648\u0627\u062f \u0628\u064a\u0626\u064a\u0629 \u0645\u0639\u064a\u0646\u0629\u060c \u0648\u0645\u0639 \u0630\u0644\u0643 \u0644\u0627 \u062a\u0648\u062c\u062f \u0625\u062d\u0635\u0627\u0626\u064a\u0627\u062a \u0645\u0641\u0635\u0644\u0629 \u0623\u0648 \u0645\u0648\u0633\u0639\u0629 \u062d\u0648\u0644 \u0627\u0646\u062a\u0634\u0627\u0631\u0647\u0627 \u0641\u064a \u0627\u0644\u0634\u0631\u0642 \u0627\u0644\u0623\u0648\u0633\u0637 \u0628\u0634\u0643\u0644 \u062e\u0627\u0635.<\/p>\r\n<p>\u064a\u062c\u062f\u0631 \u0627\u0644\u0625\u0634\u0627\u0631\u0629 \u0647\u0646\u0627 \u0625\u0644\u0649 \u0623\u0646 <a href=\"https:\/\/delta-medlab.com\/blog\/genetic-diseases-information\/\">\u0627\u0644\u0623\u0645\u0631\u0627\u0636 \u0627\u0644\u0648\u0631\u0627\u062b\u064a\u0629<\/a> \u0628\u0634\u0643\u0644 \u0639\u0627\u0645 \u0642\u062f \u062a\u0643\u0648\u0646 \u0623\u0643\u062b\u0631 \u0634\u064a\u0648\u0639\u0627\u064b \u0641\u064a \u0628\u0639\u0636 \u0627\u0644\u0645\u062c\u062a\u0645\u0639\u0627\u062a \u0627\u0644\u0645\u063a\u0644\u0642\u0629\u060c \u0623\u0648 \u0627\u0644\u062a\u064a \u062a\u062a\u0645\u064a\u0632 \u0628\u0645\u0639\u062f\u0644\u0627\u062a \u0632\u0648\u0627\u062c \u0627\u0644\u0623\u0642\u0627\u0631\u0628 \u0627\u0644\u0639\u0627\u0644\u064a\u0629 \u0648\u0647\u0648 \u0645\u0627 \u064a\u0645\u0643\u0646 \u0623\u0646 \u064a\u0632\u064a\u062f \u0645\u0646 \u0641\u0631\u0635 \u0627\u0646\u062a\u0642\u0627\u0644 \u0627\u0644\u0623\u0645\u0631\u0627\u0636 \u0627\u0644\u062c\u064a\u0646\u064a\u0629 \u0627\u0644\u0646\u0627\u062f\u0631\u0629 \u0641\u064a \u0628\u0639\u0636 \u0627\u0644\u0645\u0646\u0627\u0637\u0642. \u0648\u0646\u0630\u0643\u0631 \u0647\u0646\u0627 \u0628\u0623\u0647\u0645\u064a\u0629 \u0625\u062c\u0631\u0627\u0621 <a href=\"https:\/\/demo-website.delta-medlab.com\/%d8%a7%d9%84%d8%aa%d8%ad%d8%a7%d9%84%d9%8a%d9%84\/\/pre-marriage-tests\">\u0641\u062d\u0648\u0635\u0627\u062a \u0645\u0627 \u0642\u0628\u0644 \u0627\u0644\u0632\u0648\u0627\u062c<\/a> \u0644\u0644\u062a\u0623\u0643\u062f \u0645\u0646 \u0639\u062f\u0645 \u0648\u062c\u0648\u062f \u0637\u0641\u0631\u0627\u062a \u062c\u064a\u0646\u064a\u0629 \u0644\u0623\u064a \u0645\u0646 \u0627\u0644\u0623\u0645\u0631\u0627\u0636 \u0644\u062f\u0649 \u0623\u062d\u062f \u0627\u0644\u0634\u0631\u064a\u0643\u064a\u0646.<\/p>\r\n<h2>\u0645\u0627 \u0647\u064a \u0623\u0646\u0648\u0627\u0639 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627\u061f<\/h2>\r\n<ol>\r\n<li><strong>\u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0627\u0644\u062d\u0627\u062f\u0629<\/strong><strong>:<\/strong><\/li>\r\n<\/ol>\r\n<p>\u0648\u062a\u0624\u062b\u0631 \u0628\u0634\u0643\u0644 \u0631\u0626\u064a\u0633\u064a \u0639\u0644\u0649 \u0627\u0644\u062c\u0647\u0627\u0632 \u0627\u0644\u0639\u0635\u0628\u064a\u060c \u0648\u062a\u0633\u0628\u0628 \u0623\u0639\u0631\u0627\u0636\u0627\u064b \u062d\u0627\u062f\u0629 \u0645\u062b\u0644 \u0622\u0644\u0627\u0645 \u0627\u0644\u0628\u0637\u0646 \u0648\u0636\u0639\u0641 \u0627\u0644\u0639\u0636\u0644\u0627\u062a \u0648\u0627\u0636\u0637\u0631\u0627\u0628\u0627\u062a \u0646\u0641\u0633\u064a\u0629\u060c \u0648\u062a\u0634\u0645\u0644:<\/p>\r\n<ul>\r\n<li>\u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0627\u0644\u062d\u0627\u062f\u0629 \u0627\u0644\u0645\u062a\u0642\u0637\u0639\u0629 (Acute Intermittent Porphyria &#8211; AIP): \u0648\u0647\u064a \u0623\u0643\u062b\u0631 \u0623\u0646\u0648\u0627\u0639 \u0627\u0644\u0645\u0631\u0636 \u0627\u0644\u062d\u0627\u062f \u0634\u064a\u0648\u0639\u0627\u064b \u0648\u0647\u064a \u0646\u0627\u062a\u062c\u0629 \u0639\u0646 \u0646\u0642\u0635 \u0625\u0646\u0632\u064a\u0645 PBG deaminase.<\/li>\r\n<li>\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u062f\u0627\u0621 \u0627\u0644\u0645\u0644\u0643 (Hereditary Coproporphyria &#8211; HCP): \u0648\u0647\u064a \u0646\u0627\u062a\u062c\u0629 \u0639\u0646 \u0646\u0642\u0635 \u0625\u0646\u0632\u064a\u0645 Coproporphyrinogen oxidase \u0648\u062a\u0633\u0628\u0628 \u0623\u0639\u0631\u0627\u0636\u0627\u064b \u0639\u0635\u0628\u064a\u0629 \u0648\u0623\u062d\u064a\u0627\u0646\u0627\u064b \u062c\u0644\u062f\u064a\u0629.<\/li>\r\n<li>\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0641\u0627\u0631\u064a\u063a\u0627\u062a\u0629 (Variegate Porphyria &#8211; VP): \u062a\u062a\u0645\u064a\u0632 \u0628\u0623\u0639\u0631\u0627\u0636 \u0639\u0635\u0628\u064a\u0629 \u0648\u062c\u0644\u062f\u064a\u0629 \u0648\u062a\u0646\u062a\u062c \u0639\u0646 \u0646\u0642\u0635 \u0625\u0646\u0632\u064a\u0645 Protoporphyrinogen oxidase.<\/li>\r\n<li>\u0646\u0642\u0635 \u0646\u0627\u0632\u0639\u0629 \u0623\u0645\u064a\u0646\u0648\u0644\u064a\u0641\u0648\u0644\u064a\u0646\u0627\u062a (ALA Dehydratase Deficiency Porphyria &#8211; ADP): \u0646\u0648\u0639 \u0646\u0627\u062f\u0631 \u062c\u062f\u0627\u064b \u0646\u0627\u062a\u062c \u0639\u0646 \u0646\u0642\u0635 \u0625\u0646\u0632\u064a\u0645 ALA dehydratase.<\/li>\r\n<\/ul>\r\n<ol start=\"2\">\r\n<li><strong>\u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0627\u0644\u062c\u0644\u062f\u064a\u0629<\/strong><strong>:<\/strong><\/li>\r\n<\/ol>\r\n<p>\u062a\u0624\u062b\u0631 \u0647\u0630\u0647 \u0627\u0644\u0623\u0646\u0648\u0627\u0639 \u0628\u0634\u0643\u0644 \u0631\u0626\u064a\u0633\u064a \u0639\u0644\u0649 \u0627\u0644\u062c\u0644\u062f \u0648\u062a\u0633\u0628\u0628 \u062d\u0633\u0627\u0633\u064a\u0629 \u0634\u062f\u064a\u062f\u0629 \u0644\u0644\u0636\u0648\u0621 \u0645\u0645\u0627 \u064a\u0624\u062f\u064a \u0625\u0644\u0649 \u062a\u0642\u0631\u062d\u0627\u062a \u0648\u0628\u062b\u0648\u0631 \u0639\u0646\u062f \u0627\u0644\u062a\u0639\u0631\u0636 \u0644\u0644\u0634\u0645\u0633\u060c \u0648\u062a\u0634\u0645\u0644:<\/p>\r\n<ul>\r\n<li>\u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0627\u0644\u062c\u0644\u062f\u064a\u0629 \u0627\u0644\u0628\u0637\u064a\u0626\u0629 (Porphyria Cutanea Tarda &#8211; PCT): \u0648\u0647\u064a \u0623\u0643\u062b\u0631 \u0627\u0644\u0623\u0646\u0648\u0627\u0639 \u0627\u0644\u062c\u0644\u062f\u064a\u0629 \u0634\u064a\u0648\u0639\u0627\u064b \u0646\u0627\u062a\u062c\u0629 \u0639\u0646 \u0646\u0642\u0635 \u0625\u0646\u0632\u064a\u0645 Uroporphyrinogen decarboxylase\u060c \u0648\u063a\u0627\u0644\u0628\u0627\u064b \u0645\u0627 \u062a\u0643\u0648\u0646 \u0645\u0631\u062a\u0628\u0637\u0629 \u0628\u0627\u0644\u0639\u0648\u0627\u0645\u0644 \u0627\u0644\u0628\u064a\u0626\u064a\u0629 \u0645\u062b\u0644 \u0627\u0644\u0643\u062d\u0648\u0644 \u0648\u0623\u0645\u0631\u0627\u0636 \u0627\u0644\u0643\u0628\u062f.<\/li>\r\n<li>\u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0627\u0644\u062e\u0644\u0642\u064a\u0629 \u0627\u0644\u062c\u0644\u062f\u064a\u0629 (Congenital Erythropoietic Porphyria &#8211; CEP): \u0646\u0627\u062f\u0631\u0629 \u062c\u062f\u0627\u064b \u0648\u062a\u0633\u0628\u0628 \u062d\u0633\u0627\u0633\u064a\u0629 \u0634\u062f\u064a\u062f\u0629 \u0644\u0644\u0636\u0648\u0621 \u0648\u0647\u064a \u0646\u0627\u062a\u062c\u0629 \u0639\u0646 \u0646\u0642\u0635 \u0625\u0646\u0632\u064a\u0645 Uroporphyrinogen III synthase.<\/li>\r\n<li>\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0625\u0631\u064a\u062b\u0631\u0648\u0628\u0648\u064a\u062a\u0643 \u0628\u0631\u0648\u062a\u0648\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 (Erythropoietic Protoporphyria &#8211; EPP): \u062a\u0633\u0628\u0628 \u062d\u0633\u0627\u0633\u064a\u0629 \u0636\u0648\u0626\u064a\u0629 \u0634\u062f\u064a\u062f\u0629 \u0645\u0646\u0630 \u0627\u0644\u0637\u0641\u0648\u0644\u0629 \u0648\u062a\u0646\u062a\u062c \u0639\u0646 \u0646\u0642\u0635 \u0625\u0646\u0632\u064a\u0645 Ferrochelatase.<\/li>\r\n<li>\u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0627\u0644\u0645\u0648\u0631\u0648\u062b\u0629 \u0627\u0644\u0645\u062e\u062a\u0644\u0637\u0629 (Mixed Porphyria): \u0646\u0627\u062a\u062c\u0629 \u0639\u0646 \u0645\u0632\u064a\u062c \u0645\u0646 \u0627\u0644\u0627\u0636\u0637\u0631\u0627\u0628\u0627\u062a \u0627\u0644\u0639\u0635\u0628\u064a\u0629 \u0648\u0627\u0644\u062c\u0644\u062f\u064a\u0629 \u0648\u062a\u0624\u062b\u0631 \u0639\u0644\u0649 \u0627\u0644\u0639\u062f\u064a\u062f \u0645\u0646 \u0627\u0644\u0625\u0646\u0632\u064a\u0645\u0627\u062a.<\/li>\r\n<\/ul>\r\n<p><strong>\u062a\u0635\u0646\u064a\u0641 \u0625\u0636\u0627\u0641\u064a:<\/strong><\/p>\r\n<ol>\r\n<li>\u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0627\u0644\u0643\u0628\u062f\u064a\u0629 (Hepatic Porphyrias): \u064a\u062a\u0645 \u0641\u064a\u0647\u0627 \u0625\u0646\u062a\u0627\u062c \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0646\u0627\u062a \u0628\u0634\u0643\u0644 \u0645\u0641\u0631\u0637 \u0641\u064a \u0627\u0644\u0643\u0628\u062f (\u0645\u062b\u0644 AIP \u0648VP \u0648PCT).<\/li>\r\n<li>\u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0627\u0644\u0643\u0631\u064a\u0627\u062a \u0627\u0644\u062d\u0645\u0631 (Erythropoietic Porphyrias): \u064a\u062a\u0645 \u0641\u064a\u0647\u0627 \u0625\u0646\u062a\u0627\u062c \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0646\u0627\u062a \u0641\u064a \u0646\u062e\u0627\u0639 \u0627\u0644\u0639\u0638\u0627\u0645 (\u0645\u062b\u0644 CEP \u0648EPP).<\/li>\r\n<\/ol>\r\n<h2>\u0645\u0627 \u0647\u064a \u0623\u0639\u0631\u0627\u0636 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627\u061f<\/h2>\r\n<p>\u062a\u062e\u062a\u0644\u0641 \u0623\u0639\u0631\u0627\u0636 \u0627\u0644\u0645\u0631\u0636 \u0627\u0639\u062a\u0645\u0627\u062f\u0627\u064b \u0639\u0644\u0649 \u0627\u0644\u0646\u0648\u0639\u060c \u0648\u0644\u0643\u0646 \u064a\u0645\u0643\u0646 \u062a\u0642\u0633\u064a\u0645\u0647\u0627 \u0639\u0645\u0648\u0645\u0627\u064b \u0625\u0644\u0649 \u0623\u0639\u0631\u0627\u0636 \u0639\u0635\u0628\u064a\u0629 \u0648\u0623\u0639\u0631\u0627\u0636 \u062c\u0644\u062f\u064a\u0629:<\/p>\r\n<ol>\r\n<li><strong>\u0627\u0644\u0623\u0639\u0631\u0627\u0636 \u0627\u0644\u0639\u0635\u0628\u064a\u0629 (\u062a\u062d\u062f\u062b \u063a\u0627\u0644\u0628\u0627\u064b \u0641\u064a \u0627\u0644\u0646\u0645\u0637 \u0627\u0644\u062d\u0627\u062f): <\/strong><\/li>\r\n<\/ol>\r\n<ul>\r\n<li>\u0622\u0644\u0627\u0645 \u0634\u062f\u064a\u062f\u0629 \u0641\u064a \u0627\u0644\u0628\u0637\u0646.<\/li>\r\n<li>\u0627\u0636\u0637\u0631\u0627\u0628\u0627\u062a \u0646\u0641\u0633\u064a\u0629 \u0645\u062b\u0644 \u0627\u0644\u0642\u0644\u0642 \u0648\u0627\u0644\u0627\u0643\u062a\u0626\u0627\u0628.<\/li>\r\n<li>\u0636\u0639\u0641 \u0641\u064a \u0627\u0644\u0639\u0636\u0644\u0627\u062a.<\/li>\r\n<li>\u0627\u0636\u0637\u0631\u0627\u0628\u0627\u062a \u0641\u064a \u0627\u0644\u062c\u0647\u0627\u0632 \u0627\u0644\u0639\u0635\u0628\u064a \u0627\u0644\u0645\u0631\u0643\u0632\u064a \u0645\u062b\u0644 \u0627\u0644\u0646\u0648\u0628\u0627\u062a \u0648\u0627\u0644\u062a\u0634\u0646\u062c\u0627\u062a.<\/li>\r\n<li>\u0627\u0631\u062a\u0641\u0627\u0639 \u0641\u064a \u0636\u063a\u0637 \u0627\u0644\u062f\u0645 \u0648\u0639\u062f\u0645 \u0627\u0646\u062a\u0638\u0627\u0645 \u0646\u0628\u0636\u0627\u062a \u0627\u0644\u0642\u0644\u0628.<\/li>\r\n<\/ul>\r\n<ol start=\"2\">\r\n<li><strong>\u0627\u0644\u0623\u0639\u0631\u0627\u0636 \u0627\u0644\u062c\u0644\u062f\u064a\u0629:<\/strong><\/li>\r\n<\/ol>\r\n<ul>\r\n<li>\u062d\u0633\u0627\u0633\u064a\u0629 \u0634\u062f\u064a\u062f\u0629 \u0644\u0623\u0634\u0639\u0629 \u0627\u0644\u0634\u0645\u0633.<\/li>\r\n<li>\u062a\u0642\u0631\u062d\u0627\u062a \u062c\u0644\u062f\u064a\u0629 \u0623\u0648 \u0628\u062b\u0648\u0631.<\/li>\r\n<li>\u062a\u063a\u064a\u0631 \u0644\u0648\u0646 \u0627\u0644\u062c\u0644\u062f \u0648\u0632\u064a\u0627\u062f\u0629 \u0633\u0645\u0627\u0643\u062a\u0647.<\/li>\r\n<li>\u062a\u0635\u0628\u063a\u0627\u062a \u062f\u0627\u0643\u0646\u0629 \u0623\u0648 \u0646\u062f\u0648\u0628.<\/li>\r\n<\/ul>\r\n<h2 class=\"JlqpRe\"><span class=\"JCzEY tNxQIb\"><span class=\"CSkcDe\" dir=\"rtl\">\u0645\u0627 \u0647\u0648 \u0633\u0628\u0628 \u0645\u0631\u0636 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627\u061f<\/span><\/span><\/h2>\r\n<p>\u064a\u062d\u062f\u062b \u0627\u0644\u0645\u0631\u0636 \u0646\u062a\u064a\u062c\u0629 \u0644\u0637\u0641\u0631\u0627\u062a \u062c\u064a\u0646\u064a\u0629 \u062a\u0624\u062f\u064a \u0625\u0644\u0649 \u0646\u0642\u0635 \u0641\u064a \u0623\u062d\u062f \u0627\u0644\u0625\u0646\u0632\u064a\u0645\u0627\u062a \u0627\u0644\u0636\u0631\u0648\u0631\u064a\u0629 \u0644\u062a\u0635\u0646\u064a\u0639 \u0627\u0644\u0647\u064a\u0645\u060c \u0625\u0630 \u064a\u0645\u0643\u0646 \u0623\u0646 \u062a\u0643\u0648\u0646 \u0647\u0630\u0647 \u0627\u0644\u0637\u0641\u0631\u0627\u062a \u0645\u0648\u0631\u0648\u062b\u0629 \u0645\u0646 \u0623\u062d\u062f \u0627\u0644\u0648\u0627\u0644\u062f\u064a\u0646 \u0623\u0648 \u0645\u0646 \u0643\u0644\u0627\u0647\u0645\u0627\u060c \u0627\u0639\u062a\u0645\u0627\u062f\u0627\u064b \u0639\u0644\u0649 \u0646\u0648\u0639 \u0627\u0644\u0645\u0631\u0636. \u0639\u0644\u0627\u0648\u0629 \u0639\u0644\u0649 \u0630\u0644\u0643\u060c \u062b\u0645\u0629 \u0639\u0648\u0627\u0645\u0644 \u0623\u062e\u0631\u0649 \u064a\u0645\u0643\u0646 \u0623\u0646 \u062a\u0633\u0627\u0647\u0645 \u0641\u064a \u0638\u0647\u0648\u0631 \u0627\u0644\u0623\u0639\u0631\u0627\u0636 \u0623\u0648 \u062a\u0641\u0627\u0642\u0645\u0647\u0627 \u0645\u062b\u0644:<\/p>\r\n<ol>\r\n<li>\u0628\u0639\u0636 \u0627\u0644\u0623\u062f\u0648\u064a\u0629 (\u0645\u062b\u0644 \u0627\u0644\u0628\u0627\u0631\u0628\u064a\u062a\u064a\u0648\u0631\u0627\u062a).<\/li>\r\n<li>\u0627\u0644\u0643\u062d\u0648\u0644.<\/li>\r\n<li>\u0627\u0644\u062a\u062f\u062e\u064a\u0646.<\/li>\r\n<li>\u0627\u0644\u062c\u0648\u0639 \u0623\u0648 \u0627\u0644\u0635\u064a\u0627\u0645.<\/li>\r\n<li>\u0627\u0644\u0639\u062f\u0648\u0649 \u0623\u0648 \u0627\u0644\u062a\u0648\u062a\u0631.<\/li>\r\n<\/ol>\r\n<h2>\u0637\u0631\u0642 \u0627\u0644\u062a\u0634\u062e\u064a\u0635<\/h2>\r\n<p>\u064a\u0639\u062a\u0645\u062f \u062a\u0634\u062e\u064a\u0635 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0639\u0644\u0649 \u0639\u062f\u0629 \u062a\u062d\u0627\u0644\u064a\u0644 \u062f\u0645\u0648\u064a\u0629 \u0648\u0628\u064a\u0648\u0643\u064a\u0645\u064a\u0627\u0626\u064a\u0629 \u0644\u0644\u0643\u0634\u0641 \u0639\u0646 \u0627\u0644\u0645\u0633\u062a\u0648\u064a\u0627\u062a \u063a\u064a\u0631 \u0627\u0644\u0637\u0628\u064a\u0639\u064a\u0629 \u0645\u0646 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0646\u0627\u062a \u0623\u0648 \u0645\u0631\u0643\u0628\u0627\u062a \u0645\u0631\u062a\u0628\u0637\u0629 \u0628\u0647\u0627\u060c \u0648\u062a\u0634\u0645\u0644 \u0647\u0630\u0647 \u0627\u0644\u062a\u062d\u0627\u0644\u064a\u0644:<\/p>\r\n<ol>\r\n<li><strong>\u062a\u062d\u0644\u064a\u0644 \u0645\u0633\u062a\u0648\u064a\u0627\u062a \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0646 \u0641\u064a \u0627\u0644\u0628\u0644\u0627\u0632\u0645\u0627 (<\/strong><strong>Plasma Porphyrin Test<\/strong><strong>):<\/strong><\/li>\r\n<\/ol>\r\n<p>\u064a\u0647\u062f\u0641 \u0625\u0644\u0649 \u0642\u064a\u0627\u0633 \u062a\u0631\u0627\u0643\u0645 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0646 \u0641\u064a \u0627\u0644\u0628\u0644\u0627\u0632\u0645\u0627\u060c \u0648\u064a\u0633\u0627\u0639\u062f \u0639\u0644\u0649 \u062a\u062d\u062f\u064a\u062f \u0623\u0646\u0648\u0627\u0639 \u0645\u0639\u064a\u0646\u0629 \u0645\u0646 \u0627\u0644\u0645\u0631\u0636 \u0645\u062b\u0644 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0627\u0644\u062c\u0644\u062f\u064a\u0629.<\/p>\r\n<ol start=\"2\">\r\n<li><strong>\u062a\u062d\u0644\u064a\u0644 \u0646\u0633\u0628\u0629 \u0627\u0644\u0647\u064a\u0645\u0648\u062c\u0644\u0648\u0628\u064a\u0646 \u0648\u0627\u0644\u0647\u064a\u0645 (<\/strong><strong>Hemoglobin and Heme Tests<\/strong><strong>):<\/strong><\/li>\r\n<\/ol>\r\n<p>\u064a\u0642\u064a\u0633 \u0645\u0633\u062a\u0648\u064a\u0627\u062a \u0627\u0644\u0647\u064a\u0645 \u0627\u0644\u0630\u064a \u064a\u062a\u0643\u0648\u0646 \u0645\u0646 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0646 \u0648\u0627\u0644\u062d\u062f\u064a\u062f\u060c \u0648\u064a\u0633\u0627\u0639\u062f \u0641\u064a \u062a\u0634\u062e\u064a\u0635 \u0646\u0642\u0635 \u0627\u0644\u0625\u0646\u0632\u064a\u0645\u0627\u062a \u0627\u0644\u0645\u0633\u0624\u0648\u0644\u0629 \u0639\u0646 \u062a\u0643\u0648\u064a\u0646 \u0627\u0644\u0647\u064a\u0645.<\/p>\r\n<ol start=\"3\">\r\n<li><strong>\u062a\u062d\u0644\u064a\u0644 \u0625\u0646\u0632\u064a\u0645\u0627\u062a \u062a\u0635\u0646\u064a\u0639 \u0627\u0644\u0647\u064a\u0645 (<\/strong><strong>Enzyme Activity Test<\/strong><strong>):<\/strong><\/li>\r\n<\/ol>\r\n<p>\u064a\u064f\u0642\u0627\u0633 \u0646\u0634\u0627\u0637 \u0627\u0644\u0625\u0646\u0632\u064a\u0645\u0627\u062a \u0627\u0644\u0645\u0631\u062a\u0628\u0637\u0629 \u0628\u0639\u0645\u0644\u064a\u0629 \u062a\u0635\u0646\u064a\u0639 \u0627\u0644\u0647\u064a\u0645 \u0645\u062b\u0644 ALA dehydratase \u0648PBG deaminase \u060c \u0648\u0641\u064a \u062d\u0627\u0644 \u0646\u0642\u0635 \u0646\u0634\u0627\u0637 \u0647\u0630\u0647 \u0627\u0644\u0625\u0646\u0632\u064a\u0645\u0627\u062a \u0641\u0647\u064a \u0639\u0644\u0627\u0645\u0629 \u0639\u0644\u0649 \u0648\u062c\u0648\u062f \u0646\u0648\u0639 \u0645\u062d\u062f\u062f \u0645\u0646 \u0627\u0644\u0645\u0631\u0636.<\/p>\r\n<ol start=\"4\">\r\n<li><strong>\u062a\u062d\u0644\u064a\u0644 \u062d\u0645\u0636 \u0623\u0645\u064a\u0646\u0648\u0644\u064a\u0641\u0648\u0644\u064a\u0646\u064a\u0643 (<\/strong><strong>ALA<\/strong><strong>) \u0648\u0627\u0644\u0628\u0648\u0631\u0641\u0648\u0628\u064a\u0644\u064a\u0646\u0648\u062c\u064a\u0646 (<\/strong><strong>PBG<\/strong><strong>) \u0641\u064a \u0627\u0644\u062f\u0645:<\/strong><\/li>\r\n<\/ol>\r\n<p>\u062a\u064f\u062d\u0644\u0644 \u0645\u0633\u062a\u0648\u064a\u0627\u062a \u0647\u0630\u0647 \u0627\u0644\u0645\u0631\u0643\u0628\u0627\u062a \u0627\u0644\u062a\u064a \u062a\u062a\u0631\u0627\u0643\u0645 \u0641\u064a \u0627\u0644\u062f\u0645 \u0646\u062a\u064a\u062c\u0629 \u0644\u0646\u0642\u0635 \u0646\u0634\u0627\u0637 \u0627\u0644\u0625\u0646\u0632\u064a\u0645\u0627\u062a \u0641\u064a \u0645\u0633\u0627\u0631 \u062a\u0635\u0646\u064a\u0639 \u0627\u0644\u0647\u064a\u0645\u060c \u0648\u0627\u0631\u062a\u0641\u0627\u0639 \u0645\u0633\u062a\u0648\u064a\u0627\u062a ALA \u0648PBG \u064a\u064f\u0639\u062a\u0628\u0631 \u062f\u0644\u064a\u0644\u0627\u064b \u0642\u0648\u064a\u0627\u064b \u0639\u0644\u0649 \u0648\u062c\u0648\u062f \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0627\u0644\u062d\u0627\u062f\u0629.<\/p>\r\n<ol start=\"5\">\r\n<li><strong>\u062a\u062d\u0644\u064a\u0644 \u0627\u0644\u062c\u064a\u0646\u0627\u062a \u0627\u0644\u0648\u0631\u0627\u062b\u064a\u0629 (<\/strong><strong>Genetic Testing<\/strong><strong>):<\/strong><\/li>\r\n<\/ol>\r\n<p>\u064a\u0645\u0643\u0646 \u0625\u062c\u0631\u0627\u0621 \u0641\u062d\u0635 \u062c\u064a\u0646\u064a \u0644\u062a\u062d\u062f\u064a\u062f \u0627\u0644\u0637\u0641\u0631\u0627\u062a \u0627\u0644\u0645\u0631\u062a\u0628\u0637\u0629 \u0628\u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627\u060c \u0648\u0647\u0648 \u064a\u064f\u0633\u062a\u062e\u062f\u0645 \u0628\u0634\u0643\u0644 \u062e\u0627\u0635 \u0644\u062a\u0623\u0643\u064a\u062f \u0627\u0644\u062a\u0634\u062e\u064a\u0635 \u0641\u064a \u0627\u0644\u062d\u0627\u0644\u0627\u062a \u0627\u0644\u0645\u0634\u062a\u0628\u0647 \u0641\u064a\u0647\u0627. \u062a\u062a\u0643\u0627\u0645\u0644 \u0647\u0630\u0647 \u0627\u0644\u062a\u062d\u0627\u0644\u064a\u0644 \u0645\u0639 \u0627\u062e\u062a\u0628\u0627\u0631\u0627\u062a \u0623\u062e\u0631\u0649 \u0645\u062b\u0644 \u062a\u062d\u0644\u064a\u0644 \u0627\u0644\u0628\u0648\u0644 \u0648\u0627\u0644\u0628\u0631\u0627\u0632 \u0644\u062a\u0642\u062f\u064a\u0645 \u062a\u0634\u062e\u064a\u0635 \u062f\u0642\u064a\u0642 \u0644\u0646\u0648\u0639 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627.<\/p>\r\n<h2>\u0637\u0631\u0642 \u0627\u0644\u0639\u0644\u0627\u062c<\/h2>\r\n<p>\u064a\u0639\u062a\u0645\u062f \u0627\u0644\u0639\u0644\u0627\u062c \u0639\u0644\u0649 \u0646\u0648\u0639 \u0627\u0644\u0645\u0631\u0636 \u0648\u0634\u062f\u0629 \u0627\u0644\u0623\u0639\u0631\u0627\u0636:<\/p>\r\n<p><strong>\u064a\u062a\u0637\u0644\u0628 \u0627\u0644\u0646\u0645\u0637 \u0627\u0644\u062d\u0627\u062f \u0627\u0644\u0639\u0644\u0627\u062c \u0627\u0644\u0641\u0648\u0631\u064a \u0648\u0642\u062f \u064a\u0634\u0645\u0644:<\/strong><\/p>\r\n<ol>\r\n<li>\u0625\u0639\u0637\u0627\u0621 \u0627\u0644\u0647\u064a\u0645 \u0627\u0644\u0648\u0631\u064a\u062f\u064a (\u0647\u064a\u0645-\u0623\u0631\u062c\u064a\u0646\u064a\u062a)<strong>.<\/strong><\/li>\r\n<li>\u0639\u0644\u0627\u062c \u0627\u0644\u0623\u0639\u0631\u0627\u0636 \u0628\u0627\u0633\u062a\u062e\u062f\u0627\u0645 \u0627\u0644\u0645\u0633\u0643\u0646\u0627\u062a \u0623\u0648 \u0645\u0636\u0627\u062f\u0627\u062a \u0627\u0644\u0627\u062e\u062a\u0644\u0627\u062c<strong>.<\/strong><\/li>\r\n<li>\u062a\u062d\u0633\u064a\u0646 \u0627\u0644\u062a\u063a\u0630\u064a\u0629 \u0648\u062a\u062c\u0646\u0628 \u0627\u0644\u0635\u064a\u0627\u0645 \u0627\u0644\u0637\u0648\u064a\u0644.<\/li>\r\n<\/ol>\r\n<p><strong>\u064a\u062a\u0636\u0645\u0646 \u0639\u0644\u0627\u062c \u0627\u0644\u0646\u0645\u0637 \u0627\u0644\u062c\u0644\u062f\u064a:<\/strong><\/p>\r\n<ol>\r\n<li>\u062a\u062c\u0646\u0628 \u0627\u0644\u062a\u0639\u0631\u0636 \u0644\u0623\u0634\u0639\u0629 \u0627\u0644\u0634\u0645\u0633<strong>.<\/strong><\/li>\r\n<li>\u0627\u0644\u0641\u0635\u062f (\u0625\u0632\u0627\u0644\u0629 \u0627\u0644\u062f\u0645) \u0644\u062a\u0642\u0644\u064a\u0644 \u0645\u0633\u062a\u0648\u064a\u0627\u062a \u0627\u0644\u062d\u062f\u064a\u062f<strong>.<\/strong><\/li>\r\n<li>\u0627\u0633\u062a\u062e\u062f\u0627\u0645 \u0623\u062f\u0648\u064a\u0629 \u0645\u062b\u0644 \u0627\u0644\u0643\u0644\u0648\u0631\u0648\u0643\u064a\u0646<strong>.<\/strong><\/li>\r\n<\/ol>\r\n<h3>\u0645\u0627 \u0647\u064a \u0645\u0636\u0627\u0639\u0641\u0627\u062a \u0627\u0644\u0645\u0631\u0636\u061f<\/h3>\r\n<p>\u0625\u0630\u0627 \u0644\u0645 \u064a\u062a\u0645 \u0639\u0644\u0627\u062c \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0628\u0634\u0643\u0644 \u0635\u062d\u064a\u062d \u0641\u0642\u062f \u062a\u062a\u0641\u0627\u0642\u0645 \u0627\u0644\u0623\u0639\u0631\u0627\u0636 \u0648\u062a\u0624\u062f\u064a \u0625\u0644\u0649 \u0645\u0636\u0627\u0639\u0641\u0627\u062a \u062e\u0637\u064a\u0631\u0629\u060c \u0645\u062b\u0644:<\/p>\r\n<ol>\r\n<li>\u062a\u0644\u0641 \u062f\u0627\u0626\u0645 \u0641\u064a \u0627\u0644\u0623\u0639\u0635\u0627\u0628.<\/li>\r\n<li>\u0641\u0634\u0644 \u0643\u0644\u0648\u064a \u0623\u0648 \u0643\u0628\u062f\u064a.<\/li>\r\n<li>\u0645\u0634\u0627\u0643\u0644 \u0646\u0641\u0633\u064a\u0629 \u0637\u0648\u064a\u0644\u0629 \u0627\u0644\u0623\u0645\u062f.<\/li>\r\n<li>\u0646\u062f\u0648\u0628 \u0648\u062a\u0634\u0648\u0647\u0627\u062a \u062c\u0644\u062f\u064a\u0629.<\/li>\r\n<\/ol>\r\n<h3>\u0647\u0644 \u064a\u0645\u0643\u0646 \u0627\u0644\u0648\u0642\u0627\u064a\u0629 \u0645\u0646 \u0627\u0644\u0625\u0635\u0627\u0628\u0629 \u0628\u0647\u0627\u061f<\/h3>\r\n<p>\u0646\u0638\u0631\u0627\u064b \u0644\u0623\u0646 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0645\u0631\u0636 \u0648\u0631\u0627\u062b\u064a \u0644\u0627 \u064a\u0645\u0643\u0646 \u0627\u0644\u0648\u0642\u0627\u064a\u0629 \u0645\u0646\u0647 \u0628\u0634\u0643\u0644 \u0643\u0627\u0645\u0644\u060c \u0648\u0644\u0643\u0646 \u064a\u0645\u0643\u0646 \u062a\u0642\u0644\u064a\u0644 \u0641\u0631\u0635 \u0638\u0647\u0648\u0631 \u0627\u0644\u0623\u0639\u0631\u0627\u0636 \u0623\u0648 \u0646\u0648\u0628\u0627\u062a\u0647\u0627 \u0645\u0646 \u062e\u0644\u0627\u0644 \u062a\u062c\u0646\u0628 \u0627\u0644\u0645\u062d\u0641\u0632\u0627\u062a \u0627\u0644\u062a\u064a \u062a\u0632\u064a\u062f \u0645\u0646 \u062e\u0637\u0631 \u0627\u0644\u0646\u0648\u0628\u0627\u062a \u0627\u0644\u062d\u0627\u062f\u0629 \u0645\u062b\u0644:<\/p>\r\n<ol>\r\n<li>\u0627\u0644\u0627\u0645\u062a\u0646\u0627\u0639 \u0639\u0646 \u062a\u0646\u0627\u0648\u0644 \u0627\u0644\u0623\u062f\u0648\u064a\u0629 \u0627\u0644\u0645\u062d\u0641\u0632\u0629 \u0644\u0644\u0623\u0639\u0631\u0627\u0636.<\/li>\r\n<li>\u062a\u062c\u0646\u0628 \u0627\u0644\u0643\u062d\u0648\u0644 \u0648\u0627\u0644\u062a\u062f\u062e\u064a\u0646.<\/li>\r\n<li>\u0625\u062f\u0627\u0631\u0629 \u0627\u0644\u062a\u0648\u062a\u0631 \u0628\u0634\u0643\u0644 \u0641\u0639\u0627\u0644.<\/li>\r\n<li>\u062a\u062c\u0646\u0628 \u0627\u0644\u0635\u064a\u0627\u0645 \u0627\u0644\u0637\u0648\u064a\u0644.<\/li>\r\n<\/ol>\r\n<h3>\u0645\u0627 \u0647\u064a \u0627\u0644\u062f\u0631\u0627\u0633\u0627\u062a \u0627\u0644\u062d\u062f\u064a\u062b\u0629 \u0628\u0634\u0623\u0646 \u0647\u0630\u0627 \u0627\u0644\u0645\u0648\u0636\u0648\u0639\u061f<\/h3>\r\n<p>\u062a\u0634\u0647\u062f \u0627\u0644\u0623\u0628\u062d\u0627\u062b \u0627\u0644\u062d\u062f\u064a\u062b\u0629 \u0641\u064a \u0645\u062c\u0627\u0644 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u062a\u0637\u0648\u0631\u0627\u064b \u0641\u064a \u0645\u062c\u0627\u0644\u0627\u062a \u0627\u0644\u0639\u0644\u0627\u062c \u0627\u0644\u062c\u064a\u0646\u064a \u0648\u062a\u0637\u0648\u064a\u0631 \u0639\u0644\u0627\u062c\u0627\u062a \u062c\u062f\u064a\u062f\u0629\u060c \u0641\u0639\u0644\u0649 \u0633\u0628\u064a\u0644 \u0627\u0644\u0645\u062b\u0627\u0644 \u0647\u0646\u0627\u0643 \u062f\u0631\u0627\u0633\u0627\u062a \u062a\u062c\u0631\u064a \u062d\u0627\u0644\u064a\u0627\u064b \u062d\u0648\u0644:<\/p>\r\n<ol>\r\n<li><strong>\u0627\u0644\u0639\u0644\u0627\u062c \u0627\u0644\u062c\u064a\u0646\u064a:<\/strong> \u0644\u0627\u0633\u062a\u0628\u062f\u0627\u0644 \u0623\u0648 \u062a\u0639\u062f\u064a\u0644 \u0627\u0644\u062c\u064a\u0646\u0627\u062a \u0627\u0644\u0645\u0639\u064a\u0628\u0629 \u0627\u0644\u0645\u0633\u0624\u0648\u0644\u0629 \u0639\u0646 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627\u060c \u0648\u0647\u0648 \u0645\u0627 \u0642\u062f \u064a\u062a\u064a\u062d \u0639\u0644\u0627\u062c\u0627\u064b \u062f\u0627\u0626\u0645\u0627\u064b \u0644\u0628\u0639\u0636 \u0623\u0646\u0648\u0627\u0639 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627.<\/li>\r\n<li><strong>\u0627\u0644\u0623\u062f\u0648\u064a\u0629 \u0627\u0644\u062c\u062f\u064a\u062f\u0629:<\/strong> \u064a\u062c\u0631\u064a \u062a\u0637\u0648\u064a\u0631 \u0639\u0644\u0627\u062c\u0627\u062a \u062a\u0633\u062a\u0647\u062f\u0641 \u0627\u0644\u062c\u064a\u0646\u0627\u062a \u0648\u0627\u0644\u0625\u0646\u0632\u064a\u0645\u0627\u062a \u0627\u0644\u0645\u0633\u0624\u0648\u0644\u0629 \u0639\u0646 \u0625\u0646\u062a\u0627\u062c \u0627\u0644\u0647\u064a\u0645\u060c \u0627\u0644\u062a\u064a \u064a\u0645\u0643\u0646 \u0623\u0646 \u062a\u0642\u0644\u0644 \u0645\u0646 \u062a\u0631\u0627\u0643\u0645 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0646\u0627\u062a.<\/li>\r\n<li><strong>\u0627\u0644\u0639\u0644\u0627\u062c \u0627\u0644\u0645\u0646\u0627\u0639\u064a:<\/strong> \u064a\u062a\u0645 \u062f\u0631\u0627\u0633\u0629 \u0625\u0645\u0643\u0627\u0646\u064a\u0629 \u0627\u0633\u062a\u062e\u062f\u0627\u0645 \u0627\u0644\u0639\u0644\u0627\u062c\u0627\u062a \u0627\u0644\u0645\u0646\u0627\u0639\u064a\u0629 \u0644\u062a\u062e\u0641\u064a\u0641 \u0627\u0644\u0627\u0644\u062a\u0647\u0627\u0628\u0627\u062a \u0627\u0644\u0646\u0627\u062c\u0645\u0629 \u0639\u0646 \u062a\u0631\u0627\u0643\u0645 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0646\u0627\u062a.<\/li>\r\n<\/ol>\r\n<p>&nbsp;<\/p>\r\n<h2 class=\"wp-block-heading\">\u0647\u0644 \u062a\u062a\u0648\u0641\u0631 \u062a\u062d\u0627\u0644\u064a\u0644 \u0627\u0644\u0628\u0631\u0648\u0641\u064a\u0631\u064a\u0627 \u0641\u064a \u0645\u062e\u062a\u0628\u0631\u0627\u062a \u062f\u0644\u062a\u0627 \u0627\u0644\u0637\u0628\u064a\u0629\u061f<\/h2>\r\n<!-- \/wp:post-content -->\r\n\r\n<!-- wp:paragraph -->\r\n<p>\u0628\u0643\u0644 \u062a\u0623\u0643\u064a\u062f. \u062a\u0648\u0641\u0631 \u0645\u062e\u062a\u0628\u0631\u0627\u062a \u062f\u0644\u062a\u0627 \u0627\u0644\u0637\u0628\u064a\u0629 \u062a\u062d\u0644\u064a\u0644 \u0627\u0644\u0628\u0631\u0648\u0641\u064a\u0631\u064a\u0627 \u0625\u0644\u0649 \u062c\u0627\u0646\u0628 \u0627\u0644\u0643\u062b\u064a\u0631 \u0645\u0646 \u0627\u0644\u062a\u062d\u0627\u0644\u064a\u0644 \u0627\u0644\u062e\u0627\u0635\u0629 \u0628\u0627\u0644\u062c\u064a\u0646\u0627\u062a \u0648\u0627\u0644\u0623\u0645\u0631\u0627\u0636 \u0627\u0644\u0648\u0631\u0627\u062b\u064a\u0629 \u0627\u0644\u0645\u062a\u0648\u0641\u0631\u0629 \u0639\u0644\u0649 \u0647\u064a\u0626\u0629 \u0628\u0627\u0642\u0627\u062a \u0645\u062b\u0644 \u0628\u0627\u0642\u0629 \u062a\u062d\u0627\u0644\u064a\u0644 \u0645\u0627 \u0642\u0628\u0644 \u0627\u0644\u0632\u0648\u0627\u062c \u0623\u0648 \u062a\u062d\u0627\u0644\u064a\u0644 \u0641\u0631\u062f\u064a\u0629 \u0623\u062e\u0631\u0649.<\/p>\r\n<!-- \/wp:paragraph -->\r\n\r\n<!-- wp:paragraph -->\r\n<p>\u0643\u0645\u0627 \u062a\u062d\u0631\u0635 \u0645\u062e\u062a\u0628\u0631\u0627\u062a \u062f\u0644\u062a\u0627 \u0627\u0644\u0637\u0628\u064a\u0629 \u0641\u064a \u0627\u0644\u0633\u0639\u0648\u062f\u064a\u0629 \u0639\u0644\u0649 \u062a\u0648\u0641\u064a\u0631\u00a0<a href=\"https:\/\/backup.delta-medlab.com\/category-test-list\/tests\">\u0623\u0641\u0636\u0644 \u062e\u062f\u0645\u0627\u062a \u0627\u0644\u062a\u062d\u0627\u0644\u064a\u0644 \u0627\u0644\u0637\u0628\u064a\u0629<\/a>\u060c \u0641\u0647\u064a \u062d\u0631\u064a\u0635\u0629 \u0639\u0644\u0649 \u062a\u0642\u062f\u064a\u0645 \u0623\u0641\u0636\u0644 \u0627\u0644\u0646\u062a\u0627\u0626\u062c \u0648\u0623\u0643\u062b\u0631\u0647\u0627 \u062f\u0642\u0629\u060c \u0648\u0630\u0644\u0643 \u0645\u0646 \u062e\u0644\u0627\u0644 \u062a\u0648\u0641\u064a\u0631 \u0623\u062d\u062f\u062b \u0627\u0644\u0623\u062c\u0647\u0632\u0629 \u0648\u0623\u0643\u0641\u0623 \u0627\u0644\u0643\u0648\u0627\u062f\u0631 \u0627\u0644\u0637\u0628\u064a\u0629\u060c \u0628\u0627\u0644\u0625\u0636\u0627\u0641\u0629 \u0625\u0644\u0649 \u0627\u0644\u062a\u0632\u0627\u0645\u0647\u0627 \u0628\u0627\u0644\u0645\u0639\u0627\u064a\u064a\u0631 \u0627\u0644\u062f\u0648\u0644\u064a\u0629 \u0644\u062e\u062f\u0645\u0627\u062a \u0627\u0644\u062a\u062d\u0627\u0644\u064a\u0644 \u0627\u0644\u0637\u0628\u064a\u0629 \u0648\u0627\u0644\u0641\u062d\u0648\u0635\u0627\u062a \u0627\u0644\u0645\u062e\u0628\u0631\u064a\u0629 \u0648\u0627\u0644\u0645\u062a\u0645\u062b\u0644\u0629 \u0641\u064a\u00a0<a href=\"https:\/\/backup.delta-medlab.com\/branches\">\u062c\u0645\u064a\u0639 \u0641\u0631\u0648\u0639\u0647\u0627 \u0641\u064a \u0627\u0644\u0633\u0639\u0648\u062f\u064a\u0629<\/a>\u060c \u0623\u0648 \u0645\u0646 \u062e\u0644\u0627\u0644\u00a0<a href=\"https:\/\/backup.delta-medlab.com\/home-services\">\u062e\u062f\u0645\u0629 \u0627\u0644\u0633\u062d\u0628 \u0627\u0644\u0645\u0646\u0632\u0644\u064a<\/a>\u00a0\u0627\u0644\u062a\u064a \u062a\u0648\u0641\u0631\u0647\u0627 \u0645\u062e\u062a\u0628\u0631\u0627\u062a \u062f\u0644\u062a\u0627 \u0645\u062c\u0627\u0646\u0627\u064b.<\/p>\r\n<h3>\u00a0<\/h3>\r\n<h3>\u0627\u0644\u0645\u0631\u0627\u062c\u0639<\/h3>\r\n<p><a href=\"https:\/\/rarediseases.org\/rare-diseases\/porphyria\/%5d(https:\/rarediseases.org\/rare-diseases\/porphyria\/\">National Organization for Rare Disorders (NORD). &#8220;Porphyria&#8221;.<\/a><\/p>\r\n<p><a href=\"https:\/\/porphyriafoundation.org\/\">American Porphyria Foundation. &#8220;Types of Porphyria&#8221;.<\/a><\/p>\r\n<p>&nbsp;<\/p>","protected":false},"excerpt":{"rendered":"<p>\u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0627 \u0647\u064a \u0645\u062c\u0645\u0648\u0639\u0629 \u0645\u0646 \u0627\u0644\u0623\u0645\u0631\u0627\u0636 \u0627\u0644\u0648\u0631\u0627\u062b\u064a\u0629 \u0627\u0644\u0646\u0627\u062f\u0631\u0629 \u0627\u0644\u062a\u064a \u062a\u0646\u062a\u062c \u0639\u0646 \u062e\u0644\u0644 \u0641\u064a \u0639\u0645\u0644\u064a\u0629 \u062a\u0635\u0646\u064a\u0639 \u0627\u0644\u0647\u064a\u0645 (heme)\u060c \u0648\u0647\u0648 \u0645\u0643\u0648\u0651\u0646 \u0636\u0631\u0648\u0631\u064a \u0644\u062e\u0644\u0627\u064a\u0627 \u0627\u0644\u062f\u0645 \u0627\u0644\u062d\u0645\u0631\u0627\u0621 \u0648\u0644\u0644\u0639\u062f\u064a\u062f \u0645\u0646 \u0627\u0644\u0625\u0646\u0632\u064a\u0645\u0627\u062a \u0641\u064a \u0627\u0644\u062c\u0633\u0645. \u064a\u0639\u0648\u062f \u0633\u0628\u0628 \u0647\u0630\u0627 \u0627\u0644\u062e\u0644\u0644 \u0625\u0644\u0649 \u0646\u0642\u0635 \u0641\u064a \u0627\u0644\u0625\u0646\u0632\u064a\u0645\u0627\u062a \u0627\u0644\u0645\u0633\u0624\u0648\u0644\u0629 \u0639\u0646 \u062a\u062d\u0648\u064a\u0644 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0646\u0627\u062a \u0625\u0644\u0649 \u0627\u0644\u0647\u064a\u0645\u060c \u0645\u0645\u0627 \u064a\u0624\u062f\u064a \u0625\u0644\u0649 \u062a\u0631\u0627\u0643\u0645 \u0627\u0644\u0628\u0648\u0631\u0641\u064a\u0631\u064a\u0646\u0627\u062a \u0641\u064a \u0627\u0644\u062c\u0633\u0645 \u0627\u0644\u062a\u064a \u064a\u0645\u0643\u0646 \u0623\u0646 \u062a\u0633\u0628\u0628 \u0645\u062c\u0645\u0648\u0639\u0629 \u0645\u062a\u0646\u0648\u0639\u0629 \u0645\u0646 [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":7465,"comment_status":"open","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"footnotes":""},"categories":[68],"tags":[166,167,64,72],"class_list":["post-7317","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-diseases","tag-166","tag-167","tag-64","tag-72"],"acf":[],"_links":{"self":[{"href":"https:\/\/delta-medlab.com\/blog\/wp-json\/wp\/v2\/posts\/7317","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/delta-medlab.com\/blog\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/delta-medlab.com\/blog\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/delta-medlab.com\/blog\/wp-json\/wp\/v2\/users\/2"}],"replies":[{"embeddable":true,"href":"https:\/\/delta-medlab.com\/blog\/wp-json\/wp\/v2\/comments?post=7317"}],"version-history":[{"count":0,"href":"https:\/\/delta-medlab.com\/blog\/wp-json\/wp\/v2\/posts\/7317\/revisions"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/delta-medlab.com\/blog\/wp-json\/wp\/v2\/media\/7465"}],"wp:attachment":[{"href":"https:\/\/delta-medlab.com\/blog\/wp-json\/wp\/v2\/media?parent=7317"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/delta-medlab.com\/blog\/wp-json\/wp\/v2\/categories?post=7317"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/delta-medlab.com\/blog\/wp-json\/wp\/v2\/tags?post=7317"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}